Dichloroacetate (DCA)
Pyruvate dehydrogenase kinase inhibitor
Evidence Score
35
Inhibits PDK1-4, reactivating pyruvate dehydrogenase and forcing pyruvate into the TCA cycle. In SDH-deficient cells, this pushes metabolites into a broken TCA cycle, potentially increasing ROS and triggering apoptosis.
Succinate accumulation inhibits PHD enzymes, stabilizing HIF-1α and HIF-2α regardless of oxygen levels. This drives angiogenesis (VEGF), metabolic reprogramming (glycolysis shift), and growth factor signaling.
Upstream event:
Succinate inhibits PHD1/2/3 (α-KG-dependent dioxygenases)
Downstream effects:
Complex II dysfunction causes electron leak in the electron transport chain, increasing reactive oxygen species (ROS). This drives DNA damage but also creates a therapeutic vulnerability.
Upstream event:
Impaired electron flow through Complex II → electron leak
Downstream effects:
PDK1
Pyruvate dehydrogenase kinase 1
HIF target that suppresses pyruvate entry into TCA cycle, reinforcing glycolytic shift. Target of dichloroacetate (DCA).
UniProt: Q15118
Evidence from PubMed, OpenTargets, and ChEMBL will appear here once external data integration is enabled.
Coming in Phase 3
Have Claude analyze this drug's repurposing potential for SDH-deficient diseases.